TRANSPOSITION OF GREAT ARTERIES


This was a 36 year old lady , gravida 4 , para 1 , live 1 ( normal child ) and abortion 2 ( MTP ). She was referred for 2nd opinion for cardiac anomaly suspected only at 36 weeks of gestation. She had earlier undergone scans thrice , but no abnormality was suspected.

The following findings were seen.

Cardiomegaly with dilated left ventricle and small right ventricle were obvious. TGA _29

This is a 3 D image showing similar findings. Both pictures also show the pulmonary veins draining into left atrium and the left atrium opening into left ventricle and the right atrium opening into right ventricle. ( free wall attachment of the mitral valve leaflet,moderator band seen in the right ventricle and the tricuspid shows a septal leaflet.)

TGA_38

Mitral valve doppler flow.

TGA _2

Tricuspid doppler flow.

TGA _3

The artery coming out of left ventricle branches into two – suggestive of pulmonary artery.

TGA _15

 

 

TGA _32

The great vessel arising from the right ventricle instead of crossing runs parallel to the vessel arising from the LV.

TGA _4

 

 

TGA _6

Ventricular Septal Defect is seen.

TGA _13

 

TGA _31

 

The following picture shows a normal situs and axis . The great vessels running parallel are also seen.

TGA _9

 

TGA _10

 

In the three vessel view , single big vessel is seen in a plane.

TGA _11

3 vessel view shows only a single vessel in a given plane.

TGA _12

 

 

TGA _7

 

TGA _5

 

This shows normal veno atrial and atrial ventricular connections ( concordance ) and ventricular arterial switched connections (discordance).

The 4 chamber view showed LV to be dilated.

The great artery arising from the LV branches into two suggestive of pulmonary artery.

The great artery arising from the hypoplastic right ventricle runs parallel to the artery arising from the left ventricle.

Ventricular Septal Defect is seen .

3 Vessel trachea view show only one great vessel in a given plane.

In this patient the dilated left ventricle and the hypoplasia of the right ventricle are probably unusual findings in  Transposition of Great Arteries.

In this blog another case of T.G.A. has been reported earlier .

https://kriznanultrasoundimages.com/2013/08/25/transposition-of-the-great-arteries/

http://emedicine.medscape.com/article/900574-overview#showall

Despite its overall low prevalence, transposition of the great arteries is the most common etiology for cyanotic congenital heart disease in the newborn. This lesion presents in 5-7% of all patients with congenital heart disease. The overall annual incidence is 20-30 per 100,000 live births, and inheritance is multifactorial. Transposition of the great arteries is isolated in 90% of patients and is rarely associated with syndromes or extracardiac malformations. This congenital heart defect is more common in infants of diabetic mothers.

The primary anatomic subtypes are

(1) transposition of the great arteries with intact ventricular septum,

(2) transposition of the great arteries with ventricular septal defect,

(3) transposition of the great arteries with ventricular septal defect and left ventricular outflow tract obstruction, and

(4) transposition of the great arteries with ventricular septal defect and pulmonary vascular obstructive disease.

Differential Diagnoses

 

One thought on “TRANSPOSITION OF GREAT ARTERIES

  1. I believe that TOF is the most common cause of cyanosis in the newborn. Also am curious as to whether you were able to show the aorta connected to the small RV and whether there is conal tissue. What was final diagnosis at time of birth. Interesting case. Thanks for sharing.

    Like

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